Hereditary Angioedema

ŞEVKET ARSLAN, FATİH ÇÖLKESEN, FİLİZ SADİ AYKAN

  •  Year : 2022
  •  Vol : 2
  •  No : 1
  •  Page : 27-37
ÖZ

ABSTRACT

It is crucial to distinguish bradikinin-mediated angioedema from mast cell-mediated angioedema. Bradykinin mediated angioedema often presents with severe or even life-threatening swelling. Bradykinin-mediated angioedema does not respond to standard treatments used for mast cell-mediated angioedema. Nowadays, the development of new drugs has made it possible to treat bradykinin-mediated angioedema-related attacks and to prevent morbidity and mortality. In this article, the known and unknown aspects of bradykinin-related angioedema, its pathophysiology, diagnosis and differential diagnosis, and treatment modalities are discussed.

Key words: Bradykinin-mediated angioedema, Hereditary angioedema

Correspondence Address :
Email : [email protected]
Cite this Article As : Sadi Aykan F, Çölkesen F, Arslan Ş. Herediter Anjioödem. Mev Med Sci. 2022;2(1):27-37

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Hereditary Angioedema, Derleme,
, Vol. 2 (1)
Received :31.12.2021, Accepted : 22.03.2022, Published Online : 12.04.2022
Mevlana Medical Sciences Journal
ISSN: 2757-976X ;
E-ISSN: 2757-976X ;