In this case report, we present a four-year-old girl who was referred to our center after experiencing resistant tachycardia while being treated at another facility for fever and cough. The patient's electrocardiogram showed long RP interval supraventricular tachycardia, with negative P waves in leads D2, D3, and aVF. After transthoracic echocardiography revealed a decrease in ejection fraction, the patient was diagnosed with Permanent Junctional Reciprocal Tachycardia (PJRT). The patient did not respond to the promptly administered adenosine therapy. She was also resistant to amiodarone treatment, but was successfully treated with catheter ablation. Supraventricular tachycardia is a common condition in pediatric emergency practice and can lead to tachycardiomyopathy if diagnosis is delayed. In this case report, we emphasize the importance of carefully reassessing the ECG in cases of tachycardia that do not respond to adenosine before moving on to broad-spectrum antiarrhythmic drugs. We also highlight that PJRT should be considered in cases of resistant tachycardia and, given that it is often resistant to medication and can lead to tachycardiomyopathy, patients should be promptly referred for catheter ablation without delay.
Cite this Article As : Saraç U, Ballı Ş, Akcan HS, Baysal T, Şap F, Kılıç AO, Oflaz MB. Nadir Bir Taşikardiyomiyopati Nedeni: Permanent Junctional Resiprokan Taşikardi. Mev Med Sci. 2024; 4(3): 152-154
Conflict of interest : The authors declare that they have no conflict of interest.
Mevlana Tıp Bilimleri 2024, Vol4, Issue3 E-ISSN: 2757-976X
Received : , Accepted : , Published Online :
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