A Different Clinical Manifestation: Behçet's Disease Diagnosed with Superior Vena Cava Syndrome

ABSTRACT

Behçet's Disease (BD) is a rare autoimmune vasculitic disease that presents in many clinical conditions. While oral and genital ulcers are the most common clinical presentation, superior vena cava involvement is not common. A 38-year-old male patient was admitted to the emergency department with swelling in the face and neck that had been increasing for a few days. Bilateral internal jugular vein thrombosis was detected with Doppler ultrasonography. The patient, who had no known disease history except recurrent oral aphthae, was transferred to cardiovascular surgery due to considered Lemierre Syndrome. The patient, who developed genital ulcer during follow-up, was diagnosed with BD. We presented it because there are only a few similar cases in our literature review. We thought that this case would be an important example for considering connective tissue diseases in the differential diagnosis of patients whose clinical presentation is presented with thrombosis in an uncommon region.

Key words: Behçet’s disease, superior vena cava syndrome, venous thrombosis